Pulmonary Fibrosis
A condition where lung tissue becomes thickened and scarred, making it harder to breathe over time.
Quick Summary
Breathlessness that slowly worsens, a dry cough, tiredness and clubbing (rounding) of the fingertips.
Antifibrotic medicines to slow scarring, oxygen therapy, pulmonary rehabilitation and sometimes lung transplant.
Older age, smoking, exposure to dust or chemicals, some autoimmune conditions and certain medicines.
Overview
Pulmonary fibrosis is a type of interstitial lung disease. Scarring stiffens the lungs and makes it harder for oxygen to pass into the blood.
When no cause is found it's called idiopathic pulmonary fibrosis. Early diagnosis helps start treatment that can slow it down.
Symptoms
Breathlessness
Gradually worse, first with activity.
Dry cough
That doesn't go away.
Tiredness
And weight loss.
Finger clubbing
Rounded, wider fingertips.
Causes & Risk Factors
Biological Causes
Repeated injury to lung tissue leading to scarring; the cause is often unknown.
Key Risk Factors
- Age and smoking More common in older adults and smokers.
- Exposures Silica, asbestos, metal dust, bird droppings and mould.
- Other conditions Rheumatoid arthritis, scleroderma and some medicines.
Management & Treatment
01. Antifibrotic medicines
Can slow the scarring in some types.
02. Oxygen and rehabilitation
Help breathing and activity.
03. Lung transplant
For some people with advanced disease.
Frequently Asked Questions
How is it diagnosed?
Is it contagious?
Can it be reversed?
Sources and further reading
Last updated 21 October 2026. For more detail, see these trusted health organisations.
- Pulmonary Fibrosis(opens in a new tab) · MedlinePlus, US National Library of Medicine
- Idiopathic pulmonary fibrosis(opens in a new tab) · NHS